Congenital absence of bilateral femur is a rare congenital anomaly and usually there is a strong association with other skeletal conditions and maternal diabetes. We present an unusual case of isolated congenital bilateral femoral agenesis in non-diabetic female. A 28 years old multigravida presented for level III obstetric scan. USG demonstrated single live fetus of EGA~ 32 weeks 2 days with oligohydramnios and non-accessibility of bilateral femur. Post delivery clinical examination showed shortening of bilateral lower limb and plain x-ray confirmed absence of bilateral femur. We report this case because it does not meet the existing classification criteria for congenital femur deficiency. Proper evaluation and management of this case can help the patient and the parents to accept the condition and be able to live a good social and economically productive life.