ARCHIVES
VOL. 3, ISSUE 2 (2021)
The importance of dynamic flexion in the assessment of hirayama disease: A case series
Authors
Vignesh Muthukumaran, Mohammad Hassan, Karunya Lakshmi, Sivasubramaniyan KM, Sukrit Deo
Abstract
Introduction: Hirayama disease is a non-progressive juvenile spinal muscular atrophy of the distal upper limbs. It is a cervical myelopathy caused due to flexion movements of the neck. This is a case series of six young males presenting with atrophic changes of muscle groups involving distal upper limbs, and with Hirayama disease as their clinical diagnosis. Methods: We retrospectively reviewed cases of Hirayama disease in 6 patients referred for MR imaging to our department. We evaluated the clinical presentation and etiology of Hirayama disease based on multimodality imaging findings. Dynamic MR imaging was done in all patients to assess the degree of disease involvement of the disease. Results: In our study of 6 cases, all revealed anterior displacement of the detached posterior dura from the underlying lamina with varying degree of compression of the thecal sac. Widening of the posterior epidural space with flow voids were seen better on 3D-CISS images. Conservative management and follow up imaging were suggested in all patients. MRI is the modality of choice in establishing the diagnosis of Hirayama disease. Specifically dynamic flexion imaging is of paramount importance in the accurate depiction of imaging findings.
Download
Pages:08-10
How to cite this article:
Vignesh Muthukumaran, Mohammad Hassan, Karunya Lakshmi, Sivasubramaniyan KM, Sukrit Deo "The importance of dynamic flexion in the assessment of hirayama disease: A case series ". International Journal of Radiology Research, Vol 3, Issue 2, 2021, Pages 08-10
Download Author Certificate
Please enter the email address corresponding to this article submission to download your certificate.